Hostname: page-component-78c5997874-94fs2 Total loading time: 0 Render date: 2024-11-02T19:25:00.995Z Has data issue: false hasContentIssue false
  • English
  • Français

Infantile scimitar syndrome with severe pulmonary hypertension: successful treatment with coil embolization of the systemic arterial supply to the sequestered lung

Published online by Cambridge University Press:  19 August 2008

Jean-Pierre Pfammatter ,
Ingrid Luhmer  and
Hans Carlo Kallfelz
Jean-Pierre Pfammatter*
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Ingrid Luhmer
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Hans Carlo Kallfelz
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
*
Dr Jean-Pierre Pfammatter, MD. Division of Pediatric CardiologyChildren's Hospital, Freiburgstrasse, CH-3010 Berne, Switzerland. Fax: ++41 31 632 9748
Get access Rights & Permissions [Opens in a new window]

Abstract

Scimitar syndrome is a rare cardiopulmonary malformation. Presentation in infancy is usually associated with pulmonary hypertension and severe symptoms. We discuss treatment of such an infant. Two abnormal systemic vessels supplying the sequestered lower part of the right lung were embolized using catheter-inserted coils. The patent arterial duct was surgically ligated. These procedures resulted in a significant reduction of the shunt and the level of pulmonary hypertension, as well as in an impresssive improvement of symptoms.

Keywords

Coil embolizationpulmonary hypertensionscimitar syndrome
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 454 - 457
Copyright
Copyright © Cambridge University Press 1997

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Fisher, DR, Zuberbühler, JR.Pulmonary venous abnormalities. In: Anderson, RH, Macartney, FJ, Shinebourne, EA, Tynan, M. Pediatric Cardiology. Churchill Livingston, Edinburgh 1990; vol I, p.509Google Scholar
2.Neill, CA, Ferencz, C, Sabiston, DC, Sheldon, H. The familial occurrence of hyppoplastic right lung with systemic arterial supply and venous drainage: Scimitar syndrome. Bulletin of the J Hopkins Hospital 1960; 107: 1–21Google ScholarPubMed
3.Canter, CE, Martin, TC, Spray, TL, Weldon, CS, Strauss, AW. Scimitar syndrome in infancy. Am J Cardiol 1986; 58: 852–854.CrossRefGoogle Scholar
4.Dupuis, C, Charaf, LAC, Breviere, GM, Abou, P. Infantile form of the scimitar syndrome with pulmonary hypertension. Am J Cardiol 1993; 71: 326–330.CrossRefGoogle ScholarPubMed
5.Gao, YA, Burrows, PE, Benson, LE, Rabinovitch, M, Freedom, RM. Scimitar syndrome in. infancy. J Am Coll Cardiol 1993; 22: 873–882.CrossRefGoogle ScholarPubMed
6.Dickinson, DF, Galloway, RW, Massey, R, Sankey, R, Arnold, R. Scimitar syndrome in infancy. Role of embolization of systemic arterial supply to right lung. Br Heart J 1982; 47: 468–472.CrossRefGoogle ScholarPubMed
7.Haworth, SG, Sauer, U, Bühlmeyer, K. Pulmonary hypertension in scimitar syndrome in infancy. Br Heart J 1983; 50: 182–189.CrossRefGoogle ScholarPubMed
8.Reidy, JF, Jones, ODH, Tynan, M, Baker, EJ, Joseph, Mc. Embolisation procedures in congenital heart disease. Br Heart J 1985; 54: 184–192.CrossRefGoogle ScholarPubMed
9.Perry, SB, Radtke, W, Fellows, KE, Keane, JF, Lock, JE. Coil embolization to occlude aortopulmonary collateral vessels and shunts in patients with congenital heart disease. J Am Coll Cardiol 1989; 13: 100–108.CrossRefGoogle ScholarPubMed