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Hypoplastic left heart syndrome: multiprofessional follow-up in the mid-term following palliative procedures

Published online by Cambridge University Press:  19 August 2008

Petter S. Hagemo ,
Magnhild Rasmussen ,
Grete Bryhn  and
Inger Helena Vandvik
Petter S. Hagemo*
Affiliation:
Department of Pediatric Cardiology, Rikshospitalet, N-0027 Oslo, Norway
Magnhild Rasmussen
Affiliation:
Department of Child Neurology and Rehabilitation, Rikshospitalet, N-0027 Oslo, Norway
Grete Bryhn
Affiliation:
Department of Child Neurology and Rehabilitation, Rikshospitalet, N-0027 Oslo, Norway
Inger Helena Vandvik
Affiliation:
Department of Child and Adolescent Psychiatry, Rikshospitalet, N-0027 Oslo, Norway
*
Petter S. Hagemo, MD, Department of Pediatric Cardiology, Rikshospitalet, N-0027 Oslo, Norway. Tel: 47 2286 9076, Fax: 47 2286 9101
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Abstract

Of the 12 children who represent the complete cohort of Norwegian patients surviving the complete palliative operative programme for hypoplastic left heart syndrome, 10 were studied by a pediatric cardiologist, a pediatric neurologist, a neuropsychologist and a child psychiatrist. We found significant morbidity. Hemodynamic function was relatively uncompromised in eight of the patients, but one had significant cyanosis due to use of an operative technique subsequently abandoned and one had obstruction of the flow of blood from the left to the right atrium. Five children had disturbances of rhythm, with one requiring insertion of a pacemaker. One child had epilepsy. Delayed motor development, most often to mild degree, was found in seven children, while six had attention problems. Mental retardation was found in two children and autistic traits in one. Despite these various problems, the parents were seemingly satisfied with their own lives, and the quality of life of their children.

Keywords

Hypoplastic left heart syndromeNorwood palliationfollow-up
Type
Original Articles
Information
Cardiology in the Young , Volume 7 , Issue 3 , July 1997 , pp. 248 - 253
Copyright
Copyright © Cambridge University Press 1997

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References

1.Gutgesell, HP, Massaro, TA. Management of Hypoplastic Left Heart Syndrome in a Consortium of University Hospitals. Am J Cardiol 1995;76:809–811.CrossRefGoogle Scholar
2.Bando, K, Turrentine, MW, Sun, K, Sharp, TG, Caldwell, RL, Darragh, RK, Ensing, GJ, Cordes, TM, Flaspohler, T, Brown, JW. Surgical Managemenr of Hypoplastic Left Heart Syndrome. Ann Thorac Surg 1996;62:70–77.CrossRefGoogle ScholarPubMed
3.Lloyd, T. Prognosis of rhe Hypoplastic Left Heart Syndrome. Progress in Pediatric Cardiology 1996; 5:57–64.CrossRefGoogle Scholar
4.Rogers, BT, Msall, ME, Buck, GM, Lyon, NR, Morris, MK, Roland, JMA, Gingell, RL, Cleveland, DC, Pieroni, DR. Clinical and laboratory observations. Neurodevelopmental outcome of infants with hypoplastic left heart syndrome. The Journal of Pediatrics. 1995;126:496–498.CrossRefGoogle Scholar
5.Kern, JH, Hinton, VJ, Nereo, NE, Hayes, CJ, Gersony, WM. Developmental Outcome Following Surgery for Hypoplastic Left Heart Syndrome Circulation 1996;94(8 Suppl 1):1–652.Google Scholar
6.Norwood, WI, Lang, P, Castàeda, AR, Campbell, DN. Experience with Operations for Hypoplastic Left Heart Syndrome. J Thorac Cardiovasc Surg 1981; 82:511–519.CrossRefGoogle ScholarPubMed
7.Frankenburg, WK, Dodds, J, Archer, P, Shapiro, H, Bresnick, B. The Denver II: A major revision and restandardization of the Denver Developmental Screening Test. Pediatrics 1992; 89:91–97.CrossRefGoogle Scholar
8.Thorndike, RL, Hagen, EP, Sattler, JM. Stanford-Binet Intelligence Scale, fourth edition. Riverside, Chicago, 1986.Google Scholar
9.Bayley, N. Bayley Scales of infant development 6 (2nd ed.). The Psychological Corporation, San Antonio, 1993.Google Scholar
10.Griffiths, R. The abilities of babies. Univ. of London Press, London, 1970.Google Scholar
11.Achenbach, TM, Edelbrock, C. Manual for the Child Behavior Checklist and Revised Child Behavior Profile. Burlington, VT: University of Vermont 1991.Google Scholar
12.Achenbach, TM. III Manual for the Child Behavior Checklist/2–3 and 1992 Profile. Burlington, VT: University of Vermont 1992.Google Scholar
13.Derogatis, LR, Lipman, RS, Rickels, K, Uhlenhuth, EH, Covi, L. The Hopkins Symptom Checklist (HSCL): A self-report symptom inventory. Behav Sci 1974; 19: 1–15.CrossRefGoogle ScholarPubMed
14.Koot, HM, Verhulst, FC. Prevalence of problem behavior in Dutch children aged 2–3. Acta Psychiat Scand 1991; 83: Suppl. no.367.CrossRefGoogle Scholar
15.Manning, PB, Mayer, JE Jr, Wernovsky, G, Fishberger, SB, Walsh, EP. Staged operation to Fontan increases the incidence of sinoatrial node dysfunction. J Thorac Cardiovasc Surg 1996;111(4):833–839CrossRefGoogle ScholarPubMed
16.Glauser, TA, Rorke, LB, Weinberg, PM, Clancy, RR. Congenital Brain Anomalies Associated With the Hypoplastic Left Heart Syndrome. Pediarrics. 1990; 85:984–990.Google ScholarPubMed
17.Morris, CD, Outcalt, J, Menashe, VD. Hypoplastic left heart syndrome: Natural history in a geographically defined population. Pediatrics 1990;85:977–983.Google Scholar
18.du Plessis, AJ, Chang, AC, Wessel, DL, Lock, JE, Wernovsky, G, Newburger, JW, Mayer, JE. Cerebrovascular accidents following the Fontan operation. Pediatr Neurol 1995; 12:230–236.CrossRefGoogle ScholarPubMed
19Ferry, PC. Neurologic sequelae of open heart surgery in children: an ‘irritating question’. AJDC 1990;144:369–373.Google ScholarPubMed
20.Glauser, TA, Rorke, LB, Weinberg, PM, Clancy, RR. Acquired Neuropathologic Lesions Associated With the Hypoplastic Left Heart Syndrome. Pediatrics. 1990;85:991–1000.CrossRefGoogle ScholarPubMed
21.Fletcher, JM, Bohan, TP, Brandt, ME, Brookshire, BL, Beaver, SR, Francis, DJ, Davidson, KC, Thompson, NM, Miner, ME. Cerebral White Matter and Cognition in Hydrocephalic Children. Arch Neurol. 1992;49:818–824.Google ScholarPubMed
22.Driscoll, DJ, Offord, KP, Feldt, RH, Schaff, HV, Puga, FJ, Danielson, GK. Five-to-Fifteen Years Follow-up After Fontan Operation. Circulation 1992;85:469–496.CrossRefGoogle ScholarPubMed