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A European perspective on the management of hypoplastic left heart syndrome

Published online by Cambridge University Press:  21 September 2005

Martin J. Elliott
Affiliation:
Department of Cardiothoracic Surgery and Transplantation, The Great Ormond Street Hospital for Children NHS Trust, London, UK

Extract

Recently, the well-known American political commentator, Robert Kagan, reapplied an existing populist statement in describing Americans as being from Mars, and Europeans from Venus.1 He said “they agree on little and understand one another less and less”. In general, it would be churlish to say that this applied to the medical fraternity, but it has great resonance with intercontinental differences in the management of hypoplastic left heart syndrome. In this review, I offer a personal view of those differences, potential explanations for them, and consider how the situation may change in coming years.

Type
Norwood Procedure and Staged Palliation
Copyright
© 2004 Cambridge University Press

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References

Kagan R. Of paradise and power. New York, Knopf, 2003.
Norwood WI. Hypoplastic left heart syndrome. Cardiol Clin 1989; 7: 377385.Google Scholar
Norwood WI Jr, Jacobs ML, Murphy JD. Fontan procedure for hypoplastic left heart syndrome. Ann Thorac Surg 1992; 54: 10251029; discussion 1029–1030.Google Scholar
Norwood WI, Kirklin JK, Sanders SP. Hypoplastic left heart syndrome: experience with palliative surgery. Am J Cardiol 1980; 45: 8791.Google Scholar
Norwood WI, Lang P, Casteneda AR, Campbell DN. Experience with operations for hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 1981; 82: 511519.Google Scholar
Norwood WI, Lang P, Hansen DD. Physiologic repair of aortic atresia-hypoplastic left heart syndrome. N Engl J Med 1983; 308: 2326.Google Scholar
Norwood WI, Pigott JD. Recent advances in cardiac surgery. Pediatr Clin North Am 1985; 32: 11171124.Google Scholar
Bove EL. Surgical treatment for hypoplastic left heart syndrome. Jpn J Thorac Cardiovasc Surg 1999; 47: 4756.Google Scholar
Bove EL. Current status of staged reconstruction for hypoplastic left heart syndrome. Pediatr Cardiol 1998; 19: 308315.Google Scholar
Bove EL. Transplantation after first-stage reconstruction for hypoplastic left heart syndrome. Ann Thorac Surg 1991; 52: 701704; discussion 704–707.Google Scholar
Bove EL, Lloyd TR. Staged reconstruction for hypoplastic left heart syndrome. Contemporary results. Ann Surg 1996; 224: 387394; discussion 394–395.Google Scholar
Gaynor JW, Mahle WT, Cohen MI, Ittenbach RF, DeCampli WM, Steven JM, Nicholson SC, Spray TL. Risk factors for mortality after the Norwood procedure. Eur J Cardiothorac Surg 2002; 22: 8289.Google Scholar
Bailey L, Concepcion W, Shattuck H, Huang L. Method of heart transplantation for treatment of hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 1986; 92: 15.Google Scholar
Bailey LL. Role of cardiac replacement in the neonate. J Heart Transplant 1985; 4: 506509.Google Scholar
Bailey LL, Gundry SR. Hypoplastic left heart syndrome. Pediatr Clin North Am 1990; 37: 137150.Google Scholar
Bailey LL, Gundry SR, Razzouk AJ, Wang N, Sciolaro CM, Chiavarelli M. Bless the babies: one hundred fifteen late survivors of heart transplantation during the first year of life. The Loma Linda University Pediatric Heart Transplant Group. J Thorac Cardiovasc Surg 1993; 105: 805814; discussion 814–815.Google Scholar
Bailey LL, Nehlsen-Cannarella SL, Concepcion W, Jolley WB. Baboon-to-human cardiac xenotransplantation in a neonate. Jama 1985; 254: 33213329.Google Scholar
Bailey LL, Nehlsen-Cannarella SL, Doroshow RW, Jacobson JG, Martin RD, Allard MW, et al. Cardiac allotransplantation in newborns as therapy for hypoplastic left heart syndrome. N Engl J Med 1986; 315: 949951.Google Scholar
Boucek MM, Kanakriyeh MS, Mathis CM, Trimm RF 3rd, Bailey LL. Cardiac transplantation in infancy: donors and recipients. Loma Linda University Pediatric Heart Transplant Group. J Pediatr 1990; 116: 171176.Google Scholar
Burton PB, Hauck A, Nehlsen-Cannarella SL, Gusewitch GA, Sorensen CM, Gundry SR, et al. Hypoplastic left heart syndrome: some clues to its aetiology. Lancet 1991; 338: 1148.Google Scholar
Chiavarelli M, Gundry SR, Razzouk AJ, Bailey LL. Cardiac transplantation for infants with hypoplastic left-heart syndrome. Jama 1993; 270: 29442947.Google Scholar
Bull C, Yates R, Sarkar D, Deanfield J, de Leval M. Scientific, ethical, and logistical considerations in introducing a new operation: a retrospective cohort study from paediatric cardiac surgery. BMJ 2000; 320: 11681173.Google Scholar
Ventura SJTS, Mosher WD, Wilson JB, Henshaw S. Trends in pregnancies and pregnancy rates:estimates for the United States, 1980–1992. Monthly Vital Statistics report for NCHS 1995; 43 (11(S)): 122.Google Scholar
Sharland G, Rollings S, Simpson J, Anderson D. Hypoplastic left-heart syndrome. Lancet 2001; 357: 722.Google Scholar
Allan LD. Fetal diagnosis of fatal congenital heart disease. J Heart Lung Transplant 1993; 12 (6 Pt2): S159160.Google Scholar
Brackley KJ, Kilby MD, Wright JG, Brawn WJ, Sethia B, Stumper O, et al. Outcome after prenatal diagnosis of hypoplastic left-heart syndrome: a case series. Lancet 2000; 356: 11431147.Google Scholar
Fraisse A, Nassi C, Sigaudy S, Liprandi A, Piercecchi-Marti MD, Ligi I, et al. (Outcome of infants with hypoplastic left heart syndrome diagnosed in utero). Arch Mal Coeur Vaiss 2002; 95: 473477.Google Scholar
Allan LD, Apfel HD, Printz BF. Outcome after prenatal diagnosis of the hypoplastic left heart syndrome. Heart 1998; 79: 371373.Google Scholar
Chang R-KR, Chen AY, Klitzner TS. Clinical Management of Infants with Hypoplastic Left Heart Syndrome in the United States, 1988–1997. Pediatrics 2002; 110: 292298.Google Scholar
Plantinga RF, Frohn-Mulder IM, Takkenberg HJ, Bennink GB, Meijboom EJ, Bogers AJ. Surgical treatment of hypoplastic left heart syndrome: limited success. Ned Tijdschr Geneeskd 2001; 145: 8590.Google Scholar
Forde R, Vandvik IH. Ethical dilemmas associated with hypoplastic left-heart syndrome. Tidsskr Nor Laegeforen 1998; 118: 26492652.Google Scholar
Vandvik IH, Forde R. Ethical issues in parental decision-making. An interview study of mothers of children with hypoplastic left heart syndrome. Acta Paediatr 2000; 89: 11291133.Google Scholar
Doroshow RW. The adolescent with simple or corrected congenital heart disease. Adolesc Med 2001; 12: 122.Google Scholar
Celermajer DS, Deanfield JE. Employment and insurance for young adults with congenital heart disease. Br Heart J 1993; 69: 539543.Google Scholar
Vonder Muhll I, Cumming G, Gatzoulis MA. Risky business: insuring adults with congenital heart disease. Eur Heart J 2003; 24: 15951600.Google Scholar
Hellstedt LF. Insurability issues facing the adolescent and adult with congenital heart disease. Nurs Clin North Am 1994; 29: 331343.Google Scholar
Iannettoni MD, Bove EL, Mosca RS, Lupinetti FM, Dorostkar PC, Ludomirsky A, et al. Improving results with first-stage palliation for hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 1994; 107: 934940.Google Scholar
Sano S, Ishino K, Kawada M, Arai S, Kasahara S, Asai T, et al. Right ventricle-pulmonary artery shunt in first-stage palliation of hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 2003; 126: 504510.Google Scholar