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Double-outlet right ventricle with intact ventricular septum in a foetus with trisomy-18

Published online by Cambridge University Press:  19 August 2008

Chandrakant R. Patel*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Division of Maternal Fetal Medicine, Department of Pathology, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Kevin L. Muise
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Division of Maternal Fetal Medicine, Department of Pathology, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Raymond W Redline
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Division of Maternal Fetal Medicine, Department of Pathology, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
*
Chandrakant R. Patel, MBBS, Rainbow Babies and Childrens Hospital, Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: (216) 844 3275; Fax: (216) 844 5478

Abstract

A rare case of double-outlet right ventricle with intact ventricular septum diagnosed by foetal echocardiography at 21 weeks of gestation is described. Amniocentesis revealed trisomy–18. The cardiac diagnosis was confirmed at autopsy.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1999

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References

1.Van Praagh, S, Truman, T, Firpo, A, Bano-Rodrigo, A, Fried, R, McManus, B, Engle, MA, van Praagh, R. Cardiac malformations in trisomy–18: a study of 41 postmortem cases. J Am Coll Cardiol 1989; 13: 15861597.CrossRefGoogle ScholarPubMed
2.Ikemoto, Y, Nogi, S, Teraguchi, M, Imamura, H, Kobayashi, Y. Double-outlet right ventricle with intact ventricular septum. Acta Paediatr Jpn 1997; 39: 233236.CrossRefGoogle ScholarPubMed
3.Matsuoka, Y, Akimoto, K, Sennari, E, Hayakawa, K. Double outlet right ventricle with severe left ventricular outflow tract obstruction due to small ventricular septal defect and anomalous adherence of the mitral valve to the ventricular septum. Jpn Circ J 1987; 51: 13351340.Google Scholar
4.Accorsi, F, Thiene, G. Double-outlet right ventricle with intact interventricular septum. Case report, review of the literature and proposed pathogenetic interpretation. G Ital Cardiol 1985; 15: 232237.Google ScholarPubMed
5.Sridaromont, S, Ritter, DG, Feldt, RH, Davis, GD, Edwards, JE. Double-outlet right venrricle. Anatomic and angiocardiographic correlations. Mayo Clin Proc 1978; 53: 555577.Google ScholarPubMed
6.Gerlis, LM, Dickinson, DF, Anderson, RH. Disadvantageous closure of the interventricular communication in double-outlet right ventricle. Br Heart J 1984; 51: 670673.CrossRefGoogle ScholarPubMed
7.Bernstein, HS, Moor, P, Stanger, P, Silverman, NH. The levoatriocardinal vein: morphologic and echocardiographic identification of the pulmonary-systemic connection. J Am Coll Cardiol 1995; 26: 9951001.CrossRefGoogle Scholar