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Double orifice mitral valve associated with subaortic stenosis—echocardiographic and anatomic findings

Published online by Cambridge University Press:  19 August 2008

Thomas B. Johnson ,
Derek A. Fyfe  and
Stephen J. Swanger
Thomas B. Johnson*
Affiliation:
From the Division of Pediatric CardiologyMedical University of South Carolina, South Carolina Children's Heart Center, Charleston
Derek A. Fyfe
Affiliation:
From the Division of Pediatric CardiologyMedical University of South Carolina, South Carolina Children's Heart Center, Charleston
Stephen J. Swanger
Affiliation:
Department of Pathology and Laboratory Medicine, Medical University of South Carolina, South Carolina Children's Heart Center, Charleston
*
Dr. Thomas B. Johnson, Medical University of South Carolina, South Carolina Children's Heart Center, Division of Pediatric Cardiology, 171 Ashley Avenue, Charleston, South Carolina 29425, USA. Tel. (803) 792-3300; Fax. (803) 792-3284.
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Summary

We describe an infant with complex congenital heart disease, including double orifice of the mitral valve associated with complex subaortic stenosis. Transthoracic and intraoperative transesophageal echocardiography were used to define three distinct anatomic abnormalities, all potentially contributing to the subaortic obstruction. Stepwise surgical repair with transesophageal echocardiographic monitoring of hemodynamic function ensured optimal initial surgical results. Overwhelming postoperative complications ensued, however, and the patient died. Postmortem findings are also presented.

Keywords

Double orificesstenosisechocardiographymitral orificesubaortictransesophageal
Type
Brief Reports
Information
Cardiology in the Young , Volume 4 , Issue 2 , April 1994 , pp. 168 - 171
Copyright
Copyright © Cambridge University Press 1994

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