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Divided right atrium (‘cor triatriatum dexter’) with azygous drainage of the superior caval vein

Published online by Cambridge University Press:  19 August 2008

Eberhard G. Mühler ,
Andreas Franke  and
Bruno J. Messmer
Eberhard G. Mühler*
Affiliation:
From the Departments of Pediatric Cardiology, RWTH-Aachen, Aachen
Andreas Franke
Affiliation:
Depatments of Internal Medicine IRWTH-Aachen, Aachen
Bruno J. Messmer
Affiliation:
Depatments of Cardiovascular SurgeryRWTH-Aachen, Aachen
*
Dr. Eberhard G. Mühler, Department of Pediatric Cardiology, RWTH-Aachen, PauwelsstraKe 30, D 52057 Aachen, Germany. Tel. 49-241-8088981; Fax. 49-241-8888450.
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Summary

We describe the symptoms, the techniques for imaging and the surgical therapy in a patient with divided right atrium (‘cor triatriatum dexter’) combined with atresia of the superior caval vein. In addition to peripheral venous congestion and cyanosis, macrocephaly was the most prominent sign, the high pressure in the superior caval vein disturbing the circulation of cerebrospinal fluid. Transesophageal echocardiography was the optimal technique for imaging the dividing shelf in the right atrium. Cardiac catheterization after surgical excision of the shelf and reconstruction of the junction between the superior caval vein and the right atrium excluded any residual gradient or shunt.

Keywords

Cor triatriatum dextertransesophageal echocardiographysurgerychildren
Type
Brief Reports
Information
Cardiology in the Young , Volume 6 , Issue 1 , January 1996 , pp. 80 - 83
Copyright
Copyright © Cambridge University Press 1996

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