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Divided left atrium with totally anomalous drainage of normally connected pulmonary veins

Published online by Cambridge University Press:  29 April 2022

Robert H. Anderson Open the ORCID record for Robert H. Anderson [Opens in a new window] ,
Jeffrey P. Jacobs Open the ORCID record for Jeffrey P. Jacobs [Opens in a new window]  and
Rodney C.G. Franklin
Robert H. Anderson
Affiliation:
Cardiovascular Research Centre, Biosciences Institute, Newcastle University, Newcastle upon Tyne, UK
Jeffrey P. Jacobs*
Affiliation:
Congenital Heart Center, Division of Cardiovascular Surgery, Departments of Surgery and Pediatrics, University of Florida, Gainesville, FL, USA
Rodney C.G. Franklin
Affiliation:
Department of Paediatric Cardiology, Royal Brompton Hospital, London, UK
*
Author for correspondence: J. P. Jacobs, MD, Congenital Heart Center, UF Health Shands Hospital, Division of Cardiovascular Surgery, Departments of Surgery and Pediatrics, University of Florida, 1600 SW Archer Road, Gainesville, FL, 32608, USA. Tel: 352-273-7770; Fax: 352-392-0547. E-mail: [email protected]
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Abstract

In the December 2021 issue of Cardiology in the Young, Hubrechts and colleagues, from Brussels and Leuven in Belgium, describe their experience in which the pulmonary veins were normally connected to the morphologically left atrium. By virtue of the presence of a shelf dividing the morphologically left atrium, however, the venous return was to the morphologically right atrium, with no evidence of formation of the superior interatrial fold, meaning that there was no obstruction of flow into the systemic venous circulation. The question posed by the Belgian authors is whether the shelf dividing the morphologically left atrium is a deviated primary atrial septum, as the arrangement has previously been interpreted. As they discuss, it is currently impossible to arbitrate this conundrum. In our commentary, we discuss the background to the dilemma. We point out that, as yet, it is not possible to code accurately this congenital cardiac malformation within The International Paediatric and Congenital Cardiac Code (IPCCC), nor within the newly produced 11th Revision of the International Classification of Diseases (ICD-11).

Keywords

Pulmonary venous drainagecor triatriatum sinisternomenclaturecardiac development
Type
Commentaries
Information
Cardiology in the Young , Volume 32 , Issue 4 , April 2022 , pp. 641 - 643
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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References

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