Hostname: page-component-cd9895bd7-jkksz Total loading time: 0 Render date: 2024-12-29T11:38:00.443Z Has data issue: false hasContentIssue false

Divided left atrium associated with supravalvar mitral ring

Published online by Cambridge University Press:  19 August 2008

Silvia Álvares*
Affiliation:
Pediatric Cardiology Unit, Children's Hospital Maria Pia, Porto, Portugal
António Sá Melo
Affiliation:
Pediatric Cardiology Unit Coimbra, Portugal
Manuel Antunes
Affiliation:
Cardiothoracic Surgery Department, University Hospital, Coimbra, Portugal
*
Silvia Álvares, Consultant, Hospital de Crianças Maria Pia, Rua da Boavista 827, P–4050 Porto, Portugal. Tel: 026089900; Fax: 026000841

Abstract

Reported is a case with a rare association of divided left atrium, supramitral stenosing ring of the left atrium, connection of the left superior caval vein to the roof of the left atrium, unroofed coronary sinus with an interatrial communication at the mouth of the unroofed sinus and ventricular septal defect. The need for a complete echocardiographic examination in the presence of pulmonary venous obstruction is emphasized. Surgery was successful in spite of significant preoperative pulmonary hypertension.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1999

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Jeger, W, Gibbons, JE, Wiglesworth, FW. Cor triatriatum: clinical, hemodynamic and pathologic studies – surgical correction in early life. Pediatrics 1963; 31: 255267.Google Scholar
2.Azcarate, MJM. Obstrucciones al drenaje de las venas pulmonares. In Sanchez, PA (ed.). Cardiologia Pediatrica. Salvat, Barcelona, 1986, pp 741744.Google Scholar
3.Raghib, G, Ruttenberg, HD, Anderson, RC, Amplatz, K, Adams, P Jr, Edwards, JE. Termination of left superior vena cava in left atrium, atrial septal defect, and absence of coronary sinus: a developmental complex. Circulation 1965; 31: 906918.CrossRefGoogle ScholarPubMed
4.Ostman-Smith, I, Silverman, NH, Oldershaw, P, Lincoln, C, Shinebourne, EA. Cor triatriatum sinistrum. Diagnostic features on cross-sectional echocardiography. Br Heart J 1984; 51: 211219.Google Scholar
5.Glaser, J, Yakerivich, V, Vidne, BA. Preoperative echocardiographic diagnosis of supravalvular stenosing ring of the left atrium. Am Heart J 1984; 108: 169171.Google Scholar
6.Sullivan, ID, Robinson, PJ, Leval, M, Graham, T. Membranous supravalvular stenosis: a treatable form of congenital heart disease J Am Coll Cardiol 1986; 8: 159164.CrossRefGoogle ScholarPubMed
7.Ritter, S. Transesophageal real-time echocardiography in infants and children with congenital heart disease. J Am Coll Cardiol 1991; 8: 159164.Google Scholar
8.Shone, JD, Sellers, RD, Anderson, RC, et al. The developmental complex of ‘parachute mitral valve’, supravalvular ring of left atrium, subaortic stenosis and coarctation of the aorta. Am J Cardiol 1963; 11: 714725.Google Scholar
9.Gheissari, A, Malm, JR, Bowman, FO, Bierman, FZ. Cor triatriatum sinister: one institution's 28-year experience. Pediatr Cardiol 1992; 13: 8588.Google Scholar
10.Kirklin, JW, Barrat-Boyes, BG. Cardiac Surgery. Wiley, New York, 1986, pp 525531.Google Scholar