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Cyanosis in a patient after Fontan palliation due to unrecognised hepatic vein to coronary sinus communication

Published online by Cambridge University Press:  04 May 2021

Kristin T. Oshiro
Affiliation:
Division of Pediatric Cardiology, Columbia University Irving Medical Center/NewYork-Presbyterian Morgan Stanley Children’s Hospital, New York, NY, USA
Maria T. Thanjan
Affiliation:
Division of Pediatric Cardiology, Weill Cornell Medicine/NewYork-Presbyterian Komansky Children’s Hospital, New York, NY, USA
Ralf J. Holzer*
Affiliation:
Division of Pediatric Cardiology, Weill Cornell Medicine/NewYork-Presbyterian Komansky Children’s Hospital, New York, NY, USA
*
Author for correspondence: R. J. Holzer, MD, MSc, FACC, FSCAI, David Wallace – Starr Foundation, Professor of Pediatric Cardiology, Chief, Division of Pediatric Cardiology, Director, Pediatric Cardiac Catheterization, NewYork-Presbyterian Komansky Children’s Hospital. Weill Cornell Medicine, Department of Pediatrics, 525 East 68th Street, Room F-677. New York, NY 10065, USA. Tel: 212.746.3561; Fax: 212.746.8373. E-mail: [email protected]

Abstract

A 6-year-old male with heterotaxia, abnormal systemic and pulmonary venous drainage, and a history of Fontan completion presented with desaturations and was found by cardiac catheterisation to have a hepatic vein to coronary sinus connection. This was successfully occluded using an Amplatzer Muscular Ventricular Septal Defect Occluder.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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