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Critical obstruction of the right ventricular outflow tract by a primary hemangioendothelioma in a seven month old

Published online by Cambridge University Press:  19 August 2008

Hilary A. Robinson ,
Barry R. Keeton  and
Isabella E. Moore
Hilary A. Robinson
Affiliation:
Department of Paediatric Cardiology, Southampton University Hospitals Trust, Southampton, UK
Barry R. Keeton*
Affiliation:
Department of Paediatric Cardiology, Southampton University Hospitals Trust, Southampton, UK
Isabella E. Moore
Affiliation:
Department of Paediatric Cardiology, Southampton University Hospitals Trust, Southampton, UK
*
Dr. B. R. Keeton, Department of Paediatric Cardiology, Southampton General Hospital, Shirley, Southampton, Hants SO16 6YD, UK. Tel: 01703-796230; Fax: 01703 794526; E-mail: [email protected]
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Abstract

A 7-month-old presented with failure to thrive and a murmur. Echocardiography demonstrated a large mass in the right ventricular outflow tract, extending through the pulmonary valve. During anaesthetic induction this caused critical obstruction of the outflow tract and cardiac arrest. Pathological diagnosis showed the lesion to be a primary hemangioendothelioma. Despite surgical excision and steroid therapy, the mass continued to grow for a period of 8 weeks, but then began to regress spontaneously.

Keywords

Cardiac Haemangioendotheliomacritical outflow tract obstruction
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 2 , March 1999 , pp. 185 - 188
Copyright
Copyright © Cambridge University Press 1999

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