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Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association

Part of: Cardiac Morphology

Published online by Cambridge University Press:  24 January 2019

Neha Bansal Open the ORCID record for Neha Bansal [Opens in a new window] ,
Deemah R. Mahadin  and
Sanjeev Aggarwal
Neha Bansal*
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Deemah R. Mahadin
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Sanjeev Aggarwal
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
*
Author for correspondence: N. Bansal, MD, Division of Cardiology, Children’s Hospital of Michigan, 3901 Beaubien Blvd, Detroit, MI 48201, USA. Tel: +1(313) 745-5481; Fax: +1 313 939 0894; E-mail: [email protected]
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Abstract

Congenital complete tracheal rings are usually associated with pulmonary slings. We report a rare association of congenital complete tracheal rings with hypoplastic left heart variant. A term infant with diagnosis of a mildly hypoplastic mitral valve, unicuspid aortic valve, and moderately hypoplastic aortic arch with severe coarctation underwent a hybrid procedure initially. Upon failing extubation attempts, complete tracheal rings were seen on direct laryngoscopy. The combination of the lesions resulted in a poor outcome. In patients with failure of extubation post-cardiac surgery, a diagnosis of complete tracheal rings should be included in the differential and a direct laryngoscopy should be considered.

Keywords

Complete tracheal ringshypoplastic left heartunicuspid aortic valve
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 3 , March 2019 , pp. 445 - 447
Copyright
© Cambridge University Press 2019 

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Footnotes

Cite this article: Bansal N, Mahadin DR, Aggarwal S. (2019) Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association. Cardiology in the Young29: 445–447. doi: 10.1017/S1047951118002391

References

1. Tsai, MH, Wong, KS, Lien, R, Huang, HR, Liao, SL, Hsu, JF. Heliox as the rescue therapy for a neonate with congenital tracheal stenosis, pulmonary artery sling, and intracardiac anomalies. Am J Perinatol 2009; 26 (5): 357–360.Google Scholar
2. Chao, YC, Peng, CC, Lee, KS, Lin, SM, Chen, MR. The association of congenital tracheobronchial stenosis and cardiovascular anomalies. Int J Pediatr Otorhinolaryngol 2016; 83: 1–6.Google Scholar
3. Butler, CR, Speggiorin, S, Rijnberg, FM, et al. Outcomes of slide tracheoplasty in 101 children: a 17-year single-center experience. J Thorac Cardiovasc Surg 2014; 147 (6): 1783–1789.Google Scholar
4. Loukanov, T, Sebening, C, Springer, W, Ulmer, H, Hagl, S. Simultaneous management of congenital tracheal stenosis and cardiac anomalies in infants. J Thorac Cardiovasc Surg 2005; 130 (6): 1537–1541.Google Scholar
5. Rossi, ME, Moreddu, E, Mace, L, Triglia, JM, Nicollas, R. Surgical management of children presenting with surgical-needed tracheal stenosis. Int J Pediatr Otorhinolaryngol 2018; 108: 219–223.Google Scholar
6. Hofferberth, SC, Watters, K, Rahbar, R, Fynn-Thompson, F. Management of congenital tracheal stenosis. Pediatrics 2015; 136 (3): e660–e669.Google Scholar
7. McLaughlin, FJ, Strieder, DJ, Harris, GB, Vawter, GP, Eraklis, AJ. Tracheal bronchus: association with respiratory morbidity in childhood. J Pediatr 1985; 106 (5): 751–755.10.1016/S0022-3476(85)80348-6Google Scholar
8. Anton-Pacheco, JL, Cano, I, Garcia, A, Martinez, A, Cuadros, J, Berchi, FJ. Patterns of management of congenital tracheal stenosis. J Pediatr Surg 2003; 38 (10): 1452–1458.Google Scholar