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Atrioventricular septal defect with intact septal structures presenting as left atrioventricular valvar insufficiency

Published online by Cambridge University Press:  03 February 2006

Ulisses Alexandre Croti ,
Carlos Henrique De Marchi  and
Vera Demarchi Aiello
Ulisses Alexandre Croti
Affiliation:
Pediatric Cardiac Surgery, Hospital de Base da Faculdade de Medicina de São José do Rio Preto, São Paulo, Brazil
Carlos Henrique De Marchi
Affiliation:
Pediatric Cardiac Surgery, Hospital de Base da Faculdade de Medicina de São José do Rio Preto, São Paulo, Brazil
Vera Demarchi Aiello
Affiliation:
Laboratory of Pathology, Heart Institute (InCor), University of São Paulo Medical School, São Paulo, Brazil
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Abstract

We describe the findings in a six-year-old girl who presented with signs of left atrioventricular valvar insufficiency. The echocardiogram showed a common atrioventricular junction, intact atrial and ventricular septal structures. At surgery, the left-sided atrioventricular valve was found to be tri-foliate, and corrected by valvoplasty. To the best of our knowledge, this is the first case of atrioventricular septal defect with common atrioventricular junction and intact septal structures diagnosed during life.

Keywords

Atrioventricular canal malformationcongenital heart defectvalvoplasty
Type
Brief Report
Information
Cardiology in the Young , Volume 16 , Issue 1 , January 2006 , pp. 92 - 94
Copyright
© 2006 Cambridge University Press

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