Published online by Cambridge University Press: 19 August 2008
We describe a neonate who presented with aortic atresia, a hypoplastic left ventricle and aorto-left ventricular tunnel. These findings, recognized by transthoracic and transesophageal cross-sectional echocardiography complemented by Doppler color flow imaging, were confirmed at surgery by direct inspection. This complex of associations has not been described before and suggests a primary abnormality of the left ventricle because diastolic filling from the aorto-left venticular tunnel and mitral flow should tend to ensure fetal left ventricular growth.