Hostname: page-component-669899f699-b58lm Total loading time: 0 Render date: 2025-04-24T15:00:06.475Z Has data issue: false hasContentIssue false
  • English
  • Français

Aortic valvar atresia with a normal-sized left ventricle in an adolescent

Published online by Cambridge University Press:  03 January 2024

Sourabh Goswami ,
Rengarajan Rajagopal Open the ORCID record for Rengarajan Rajagopal [Opens in a new window]  and
Surender Deora
Sourabh Goswami
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
Rengarajan Rajagopal*
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
Surender Deora
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
*
Corresponding author: Rengarajan Rajagopal; Email: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Atresia of the aortic valve is usually associated with hypoplasia of the mitral valve and the left ventricle. In very rare cases, a ventricular septal defect may be associated with aortic atresia, when left ventricle and mitral valve are normal-sized, due to the presence of an outflow for the left ventricle through the ventricular septal defect. We present the multi-modality imaging findings of an adolescent girl who presented with breathlessness and was later found to have aortic valvar atresia with a normal-sized left ventricle.

Keywords

aortic valveaortic atresiacongenital heart disease
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 2 , February 2024 , pp. 462 - 464
Check for updates
Copyright
© The Author(s), 2024. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Article purchase

Temporarily unavailable

References

Rudolph, AM, Heymann, MA, Spitznas, U. Hemodynamic considerations in the development of narrowing of the aorta. Am J Cardiol 1972; 30: 514–525. DOI: 10.1016/0002-9149(72)90042-2.CrossRefGoogle ScholarPubMed
Bardo, DM, Frankel, DG, Applegate, KE, Murphy, DJ, Saneto, RP. Hypoplastic left heart syndrome. Radiographics 2001; 21: 705–717.CrossRefGoogle ScholarPubMed
Noonan, JA, Nadas, AS. The hypoplastic left heart syndrome: an analysis of 101 cases. Pediatr Clin North Am 1958; 5: 1029–1056.CrossRefGoogle ScholarPubMed
Anderson, RH, Crucean, A, Spicer, DE. What is the hypoplastic left heart syndrome? J Cardiovasc Dev Dis 2023; 10: 133.Google ScholarPubMed
Roberts, WC, Perry, LW, Chandra, RS, Meyers, GE, Shapiro, SR, Scott, LP. Aortic valve atresia: a new classification based on necropsy study of 73 cases. Am J Cardiol 1976; 37: 753–756.CrossRefGoogle ScholarPubMed
Freedom, RM, Williams, WG, Dische, MR, Rowe, RD. Anatomical variants in aortic atresia. Potential candidates for ventriculoaortic reconstitution. Br Heart J 1976; 38: 821–826.CrossRefGoogle ScholarPubMed
Jagia, P, Sharma, A, Gupta, SK, Guleria, M. Aortic atresia with normal sized left ventricle. Indian J Radiol Imaging 2016; 26: 521–523.Google ScholarPubMed
Esmaeilzadeh, M, Naderi, N, Tabaei, AS. Aortic atresia with normally developed left ventricle in a young adult. Cardiol J 2011; 18: 304–306.Google ScholarPubMed
Li, W, Li, J, Chen, X. A rare case of congenital heart disease: anomalous origin of coronary artery from innominate artery with coronary fistula and truncus arteriosus. Cardiol Young 2021; 31: 1345–1347.CrossRefGoogle ScholarPubMed
Bernhard, WF, Poirier, V, LaFarge, CG. Relief of congenital obstruction to left ventricular outflow with a ventricular-arotic prosthesis. J Thorac Cardiovasc Surg 1975; 69: 223–229.CrossRefGoogle ScholarPubMed
Freedom, RM, Culham, JAG, Rowe, RD. Aortic atresia with normal left ventricle distinctive angiocardiographic findings. Cathet Cardiovasc Diagn 1977; 3: 283–295.CrossRefGoogle ScholarPubMed
Perry, LW, Scott, LP, Shapiro, SR, Chandra, RS, Roberts, WC. Atresia of the aortic valve with ventricular septal defect. Chest 1977; 72: 757–761.CrossRefGoogle ScholarPubMed
Thiene, G, Gallucci, V, Macartney, FJ, Torso, SD, Pellegrino, PA, Anderson, RH. Anatomy of aortic atresia. Circulation 1979; 59: 173–178.CrossRefGoogle ScholarPubMed
Nathan, M, Rimmer, D, del Nido, PJ, et al. Aortic atresia or severe left ventricular outflow tract obstruction with ventricular septal defect: results of primary biventricular repair in neonates. Ann Thorac Surg 2006; 82: 2227–2232.CrossRefGoogle ScholarPubMed