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Aortic atresia with normal left ventricle and intact ventricular septum—a major form of subaortic stenosis complicating an atrioventricular septal defect with intact septal structures

Published online by Cambridge University Press:  19 August 2008

Lucile Houyel ,
Véronique Zupana  and
Françoise Roset
Lucile Houyel*
Affiliation:
From the Marie-Lannelongue Hospital, Béclère Hospital, Clamart
Véronique Zupana
Affiliation:
Paris-Sud University, Paris and the Neonatal Intensive Care Unit and Pathology DepartmentBéclère Hospital, Clamart
Françoise Roset
Affiliation:
Paris-Sud University, Paris and the Neonatal Intensive Care Unit and Pathology DepartmentBéclère Hospital, Clamart
*
Dr. Lucile Houyel, Hôpital Marie-Lannelongue, 133 avenue de la Résistance, 92350 Le Plessis-Robinson, France. Tel. (1) 40 94 28 00; Fax. (1)46303792.
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Summary

We report an unusual form of aortic atresia with a normal sized left ventricle, intact ventricular septum and isolated cleft of the left atrioventricular valve, with abnormal attachments creating both subaortic atresia and massive regurgitation across the left atrioventricular valve. This combination, never described before as far as we are aware, can be considered as an extreme form of subaortic stenosis complicating a very particular type of atrioventricular septal defect.

Keywords

Aortic atresiaisolated cleft left atrioventricular valvesubaortic stenosis
Type
Brief Reports
Information
Cardiology in the Young , Volume 5 , Issue 3 , July 1995 , pp. 282 - 285
Copyright
Copyright © Cambridge University Press 1995

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