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Absent pulmonary valve in tricuspid atresia with left ventricular outflow tract obstruction and patent arterial duct

Published online by Cambridge University Press:  19 August 2008

Robert P. Lemke ,
Neils G. Giddins  and
Jonah N.K. Odim
Robert P. Lemke
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
Neils G. Giddins
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
Jonah N.K. Odim*
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
*
Dr Jonah N.K. Odim, Director, Pediatric Cardiac Surgery, 685 William Avenue, Winnipeg, Manitoba, Canada, R3E 0Z2. Tel: (204) 787 2412, Fax: (204) 787 1419.
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Abstract

We describe a neonate with tricuspid atresia, absent pulmonary valve, right ventricular hypoplasia, small venrricular septal defect, left ventricular ourflow tract obstruction and a patent arterial duct. These finding were diagnosed by echocardiography and confirmed by cardiac catherterization and postmortem examination. This is a unique report of a functionally single ventricle variant of absent pulmonary valve syndrome and biventricular outlet obstuction.

Keywords

Absent pulmonary valve synfrometricuspid atresiapatent arterial duct
Type
Brief Report
Information
Cardiology in the Young , Volume 7 , Issue 1 , January 1997 , pp. 94 - 97
Copyright
Copyright © Cambridge University Press 1997

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