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Unguarded mitral orifice, mirror-imaged atrial arrangement, and discordant atrioventricular connections

Published online by Cambridge University Press:  19 August 2008

Satoshi Yasukochi ,
Gengi Satomi ,
Insam Park ,
Masahiko Ando  and
Kazuo Momma
Satoshi Yasukochi*
Affiliation:
Department of Pediatric Cardiology, Nagano Children's Hospital, Nagano, Japan
Gengi Satomi
Affiliation:
Department of Pediatric Cardiology, Nagano Children's Hospital, Nagano, Japan
Insam Park
Affiliation:
Department of Pediatric Cardiology, The Heart Institute of Japan, Tokyo Women's Medical College, Tokyo, Japan
Masahiko Ando
Affiliation:
Department of Pediatric Cardiology, The Heart Institute of Japan, Tokyo Women's Medical College, Tokyo, Japan
Kazuo Momma
Affiliation:
Department of Pediatric Cardiology, The Heart Institute of Japan, Tokyo Women's Medical College, Tokyo, Japan
*
Satoshi Yasukochi, M.D., Department of Pediatric Cardiology, Nagano Children's Hospital, 3100 Toyoshina, Toyoshina, Nagano 399–8288, Japan. Tel: +81–263–73–6700; Fax: +81–263–73–5432; E-mail: [email protected]
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Abstract

We report two autopsy proven cases of unguarded mitral orifice associated with mirror-imaged atrial arrangement, discordant atrioventricular connections, double outlet right ventricle, pulmonary valvar stenosis or atresia, and atrialisation of the morphologically left ventricle. The morphologically left atrioventricular junction was devoid of valvar leaflets, and there was no tension apparatus within the ventricle. To the best of our knowledge, this is the first description of this rare cardiac malformation

Keywords

Unguarded mitral orificedouble outlet right ventriclesegmental combination
Type
Original Articles
Information
Cardiology in the Young , Volume 9 , Issue 5 , September 1999 , pp. 478 - 483
Copyright
Copyright © Cambridge University Press 1999

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