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Transposition of the great arteries with an intact ventricular septum in older children

Published online by Cambridge University Press:  26 December 2024

Xiaowei Zhou ,
Fanyan Luo  and
Haisong Bu Open the ORCID record for Haisong Bu [Opens in a new window]
Xiaowei Zhou
Affiliation:
Department of Cardiovascular Surgery, Xiangya Hospital, Central South University, Changsha, China
Fanyan Luo
Affiliation:
Department of Cardiovascular Surgery, Xiangya Hospital, Central South University, Changsha, China
Haisong Bu*
Affiliation:
Department of Cardiovascular Surgery, Xiangya Hospital, Central South University, Changsha, China
*
Corresponding author: Haisong Bu; Email: [email protected]
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Abstract

Complete transposition of the great arteries is a common life-threatening complex cyanotic congenital heart disease in infants, resulting in the operation usually performed about one week after birth. However, little is known about the surgical strategy and experience of transposition of the great arteries with an intact ventricular septum in older patients. Herein, we present an abandoned 7-year-old boy with severe cyanosis with clubbed fingers and toes and then diagnosed with transposition of the great arteries with an intact ventricular septum, atrial septal defect, patent ductus arteriosus, and pulmonary hypertension. The patient underwent a two-staged procedure: an aortopulmonary shunt and pulmonary artery banding were performed at the first stage, followed by the Switch operation, defect repair, and patent ductus arteriosus ligation, all of which were successfully performed. The patient was discharged on the 15th day after the operation, and the arterial oxygen saturation returned to normal level (99%). The illustrative report highlights the essence of raising awareness and developing accurate treatment strategy of transposition of the great arteries, especially in remote rural areas of eastern countries, where the level of health care and services is relatively underdeveloped.

Keywords

Transposition of the great arteriesintact ventricular septumolder childrensurgeryhealth care and services
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 12 , December 2024 , pp. 2698 - 2702
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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