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Systemic hypertension in an infant with unrepaired tetralogy of Fallot: case report

Published online by Cambridge University Press:  13 November 2012

Michael Khoury ,
Michael Kallile ,
Joseph May  and
Rajesh Punn
Michael Khoury
Affiliation:
Department of Paediatrics, The Hospital for Sick Children, Toronto, Ontario, Canada
Michael Kallile
Affiliation:
Division of Pediatric Cardiology, Lucile Packard Children's Hospital, Palo Alto, CA, United States of America
Joseph May
Affiliation:
Division of Pediatric Cardiology, Lucile Packard Children's Hospital, Palo Alto, CA, United States of America
Rajesh Punn*
Affiliation:
Division of Pediatric Cardiology, Lucile Packard Children's Hospital, Palo Alto, CA, United States of America
*
Correspondence to: Dr R. Punn, MD, Division of Pediatric Cardiology, Lucile Packard Children's Hospital, 750 Welch Road, Suite no. 305, Palo Alto, CA 94304, United States of America. Tel: +1 650 498 4563; Fax: +1 650 725 8343; E-mail: [email protected]
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Abstract

Patients with severe right ventricular outflow tract obstruction in tetralogy of Fallot typically have right-to-left shunting, resulting in low pulmonary blood flow and cyanosis. Here we present the case of an infant with tetralogy of Fallot and severe pulmonary valve stenosis, complicated by systemic hypertension, the presence of which altered flow dynamics and possibly prevented cyanosis.

Keywords

Tetralogy of fallothypertensionsystemic vascular resistance
Type
Brief Reports
Information
Cardiology in the Young , Volume 23 , Issue 5 , October 2013 , pp. 746 - 748
Copyright
Copyright © Cambridge University Press 2012 

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