Hostname: page-component-586b7cd67f-tf8b9 Total loading time: 0 Render date: 2024-11-24T13:24:53.197Z Has data issue: false hasContentIssue false
  • English
  • Français

Surgical ablation of a cardiac rhabdomyoma in an infant with tuberous sclerosis

Published online by Cambridge University Press:  19 August 2008

Dagmar Henglein ,
Nabil-Maurice Guirgis  and
Gérard Bloch
Dagmar Henglein*
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Nabil-Maurice Guirgis
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Gérard Bloch
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
*
Dr Dagmar Henglein, Hôpital Lariboisière, 6 rue Ambroise Paré, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France. Tel: 33-1-49 95 65 91 (secretary), Tel 31-49 95 84 54 (direct), Fax 33-1-49 95 86 32
Get access Rights & Permissions [Opens in a new window]

Abstract

Cardiac rhabdomyoma is a rare tumor. Because of its rate of regression, mainly in the first year of life, conservative therapy is generally suggested when diagnosis occurs in infancy. We report surgical ablation of a rhabdomyoma in a 2-month-old boy in whom the tumor extended into the subaortic outflow tract. The tumor, which had a dual attachment to the aortic and mitral valves, was safely removed without any valvar damage. We suggest immediate surgical intervention for those rhabdomyomas which are life-threatening because of their size, location, or arrhythmogenicity.

Keywords

RhabdomyomaCardiac tumor in infancy
Type
Brief Reports
Information
Cardiology in the Young , Volume 8 , Issue 1 , January 1998 , pp. 134 - 135
Copyright
Copyright © Cambridge University Press 1998

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1Webb, DW, Thomas, RD, Osborne, JP. Cardiac rhabdomyomas and their association with tuberous sclerosis. Arch Dis Child 1993;68(3): 367–370.CrossRefGoogle ScholarPubMed
2. Arciniegas, E, Hakimi, M, Farooki, ZQ, Truccone, NJ, Green, EW. Primary cardiac tumors in children. J Thorac Cardiovasc Surg 1980;79(4): 582–591.CrossRefGoogle ScholarPubMed
3. Werner, H Jr, Mirlesse, V, Jacquemard, F, Sonigo, P, Delezoide, AL, Gonzales, M, Brunelle, F, Fermont, L, Daffos, F. Prenatal diagnosis of toberous sclerosis. Use of magnetic resonance, imaging and its implications for prognosis. Prenatal Diag 1994; 14(12): 1151–1154.CrossRefGoogle ScholarPubMed
4. Shepherd, CW, Gomez, MR, Lie, JT, Crowson, CS. Causes of death in patients with tuberous sclerosis. Mayo Clinic Proceedings 1991;66(8): 792–796.CrossRefGoogle ScholarPubMed
5. Soria, F, Valdes, M, Garcia, A, Vicente, T, Perez, F, Garcia, J, Cano, A, Roldan, D. The spontaneous regression of a rhabdomyoma of the right ventricle. Rev Espan Cardiol 1991;44(3): 203–206.Google ScholarPubMed
6. Spooner, EW, Farina, MA, Shaher, RM, Foster, ED. Left ventricular rhabdomyoma causing subaortic stenosis - two dimensional echocardiographic appearance. Pediat Cardiol 1982;2: 67–71.CrossRefGoogle ScholarPubMed
7. Nir, A, Tajik, AJ, Freeman, WK, Seward, JB, Offord, KP, Edwards, WD, Mair, DD, Gomez, MR. Tuberous sclerosis and cardiac rhabdomyoma. Amer J Cardiol 1995;76(5): 419–421.CrossRefGoogle ScholarPubMed
8. Muhler, EG, Turniski-Harder, V, Engelhardt, W, von Bernuth, G. Cardiac involvement in tuberous sclerosis. Br Heart J 1994;72(6):584–590.CrossRefGoogle ScholarPubMed
9. Bjorkhem, G, Lundstrom, NR, Lingman, GIntracardiac rhabdomyomas in neonates: report of three cases. Acta Paediat 1992;81(9):712–715.CrossRefGoogle ScholarPubMed
10. Watson, GH. Cardiac rhabdomyomas in tuberous sclerosis. AnnNYAcadSci 1991;615: 50–57.CrossRefGoogle ScholarPubMed