Hostname: page-component-586b7cd67f-rcrh6 Total loading time: 0 Render date: 2024-11-24T19:47:26.956Z Has data issue: false hasContentIssue false

Septum primum malposition defect and inferior sinus venosus defect: a rare association

Published online by Cambridge University Press:  02 October 2014

Deepa Prasad
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
Christopher Snyder
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
Ravi Ashwath*
Affiliation:
Case Western Reserve University, Rainbow Babies and Children’s Hospital, Cleveland, Ohio, United States of America
*
Correspondence to: R. Ashwath, MD, Division of Pediatric Cardiology, Rainbow Babies and Children’s Hospital, 11100 Euclid Avenue, MS RBC 6011, Cleveland, OH 44106, United States of America. Tel: +216 844 3528; Fax: +216 201 4650; E-mail: [email protected]

Abstract

We present a case of a 2-year-old girl who presented with respiratory distress and umbilical abscess, and was found to have an inferior sinus venosus defect, malposition of the atrial septum primum, absent septum secundum, and anomalous drainage of the right upper and lower pulmonary veins to the right atrium.

Type
Brief Reports
Copyright
© Cambridge University Press 2014 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Valente, AM, Sena, L, Powell, AJ, Del Nido, PJ, Geva, T. Cardiac magnetic resonance imaging evaluation of sinus venosus defects: comparison to surgical findings. Pediatr Cardiol 2007; 28: 5156.CrossRefGoogle ScholarPubMed
2. Ettedgui, JA, Siewers, RD, Zuberbuhler, JR, Anderson, RH. Echocardiographic diagnosis of inferior sinus venosus defects. Cardiol Young 1992; 2: 338341.Google Scholar
4. Muñoz-Castellanos, L, Espinola-Zavaleta, N, Kuri-Nivón, M, Ruiz, JF, Keirns, C. Atrial septal defect: anatomoechocardiographic correlation. J Am Soc Echocardiogr 2006; 19: 11821189.Google Scholar
5. Attenhofer Jost, CH, Connolly, HM, Danielson, GK, et al. Sinus venosus atrial septal defect: long-term postoperative outcome for 115 patients. Circulation 2005; 112: 19531958.Google Scholar
3. Crystal, MA, Al Najashi, K, Williams, WG, Redington, AN, Anderson, RH. Inferior sinus venosus defect: echocardiographic diagnosis and surgical approach. J Thorac Cardiovasc Surg 2009; 137: 13491355.Google Scholar
6. Banka, P, Bacha, E, Powell, A, Benavidez, O, Geva, T. Outcomes of inferior sinus venosus defect repair. J Thorac Cardiovasc Surg 2011; 142: 517522.Google Scholar
7. Plymale, J, Kolinski, K, Frommelt, P, Bartz, P, Tweddell, J. Earing MG inferior sinus venosus defects: anatomic features and echocardiographic correlates. Pediatr Cardiol 2013; 34: 322326.Google Scholar
8. Prompona, M, Muehling, O, Naebauer, M, Schoenberg, SO, Reiser, M, Huber, A. MRI for detection of anomalous pulmonary venous drainage in patients with sinus venosus atrial septal defects. Int J Cardiovasc Imaging 2011; 27: 403412.Google Scholar
9. Kivistö, S, Hänninen, H, Holmström, M. Partial anomalous pulmonary venous return and atrial septal defect in adult patients detected with 128-slice multidetector computed tomography. J Cardiothorac Surg 2011; 6: 126.Google Scholar
10. Beerbaum, P, Parish, V, Bell, A, Gieseke, J, Körperich, H, Sarikouch, S. Atypical atrial septal defects in children: noninvasive evaluation by cardiac MRI. Pediatr Radiol 2008; 38: 11881194.CrossRefGoogle ScholarPubMed
11. Sturm, JT, Ankeney, JL. Surgical repair of inferior sinus venosus atrial septal defect. J Thorac Cardiovasc Surg 1979; 78: 570572.Google Scholar
12. Perna, AM, Alajmo, F. Partial anomalous pulmonary venous return of an uncommon type. J Cardiovasc Surg 1984; 25: 563565.Google Scholar
13. Van Praagh, S, Carrera, ME, Sanders, S, Mayer, JE Jr, Van Praagh, R. Partial or total direct pulmonary venous drainage to right atrium due to malposition of septum primum. Chest 1995; 107: 14881498.Google Scholar
14. Tomar, M, Radhakrishnan, S, Shrivastava, S. Partial or total anomalous pulmonary venous drainage caused by malposition of septum primum: echocardiographic description of a rare variant of anomalous pulmonary venous drainage. J Am Soc Echocardiogr 2005; 18: 884.Google Scholar
15. Hiramatsu, T, Takanashi, Y, Imai, Y, et al. Atrial septal displacement for repair of anomalous pulmonary venous return into the right atrium. Ann Thorac Surg 1998; 65: 11101114.CrossRefGoogle ScholarPubMed