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Normalisation of left ventricular systolic function after change from VVI pacing to biventricular pacing in a child with congenital complete atrioventricular block, long-QT syndrome, and congenital muscular dystrophy: a 10-year follow-up

Published online by Cambridge University Press:  17 May 2013

Sabrina G. Ellesøe ,
Jesper I. Reimers  and
Henrik Ø. Andersen
Sabrina G. Ellesøe*
Affiliation:
Department of Disease Systems Biology, University of Copenhagen, Denmark
Jesper I. Reimers
Affiliation:
Deptartment of Cardiology, Rigshospitalet, Copenhagen, Denmark
Henrik Ø. Andersen
Affiliation:
Deptartment of Cardio Thoracic Surgery, Rigshospitalet, Copenhagen, Denmark
*
Correspondence to: S. G. Ellesøe, Blegdamsvej 3b, lok. 6.2.19, 2200 Copenhagen, Denmark. Tel: 0045 35325039; Fax: 0045 35 32 50 01; E-mail: [email protected]
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Abstract

Development of dilated cardiomyopathy in patients with congenital complete atrioventricular block with or without pacemaker is well described. We report a case of dilated cardiomyopathy in a child with congenital complete atrioventricular block, long-QT syndrome, and VVI pacemaker. Temporary pacing in the right ventricular outflow tract demonstrated a 63% increase in cardiac output. After change to biventricular DDD pacing, left ventricular systolic function and diastolic dimensions normalised.

Keywords

Dilated cardiomyopathycongenital complete atrioventricular blockpacemakerbiventricularSmith–Magenis syndromecongenital muscular dystrophy
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 3 , June 2014 , pp. 520 - 523
Copyright
Copyright © Cambridge University Press 2013 

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