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Meandering right pulmonary vein associated with severe and progressive “idiopathic-like” pulmonary hypertensive vascular disease

Published online by Cambridge University Press:  16 September 2015

Sofia Cuenca Open the ORCID record for Sofia Cuenca [Opens in a new window] ,
Montserrat Bret  and
Maria Jesus del Cerro
Sofia Cuenca*
Affiliation:
Cardiology Department, Hospital Universitario Puerta de Hierro Majadahonda, Madrid, Spain
Montserrat Bret
Affiliation:
Pediatric Radiology Department, Hospital Universitario La Paz, Madrid, Spain
Maria Jesus del Cerro
Affiliation:
Pediatric Cardiology Department, Hospital Universitario Ramon y Cajal, Madrid, Spain
*
Correspondence to: S. Cuenca, Cardiology Department, Hospital Universitario Puerta de Hierro Majadahonda, Manuel de Falla 1, Majadahonda, Madrid 28222, Spain. Tel: +34 913369027; Fax: +34 913368685; E-mail: [email protected]
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Abstract

Congenital anomalies of the pulmonary veins are rare. Meandering right pulmonary vein, considered a part of the Scimitar syndrome spectrum, is often an incidental finding during chest imaging. We present the case of a 4-year-old girl diagnosed with meandering pulmonary vein, who developed pulmonary hypertensive disease with an aggressive course, in spite of absence of hypoxia or elevated pulmonary wedge pressure.

Keywords

Meandering pulmonary veinscimitar syndromepulmonary hypertension
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Supplement 3 , March 2016 , pp. 615 - 618
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Copyright
© Cambridge University Press 2015 

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References

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