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Everolimus treatment of a newborn with rhabdomyoma causing severe arrhythmia

Published online by Cambridge University Press:  20 November 2014

Funda Öztunç ,
Sezen U. Atik  and
Aslı O. Güneş
Funda Öztunç
Affiliation:
Department of Pediatric Cardiology, Cerrahpaşa Medical Faculty, Istanbul University, Istanbul, Turkey
Sezen U. Atik*
Affiliation:
Department of Pediatric Cardiology, Cerrahpaşa Medical Faculty, Istanbul University, Istanbul, Turkey
Aslı O. Güneş
Affiliation:
Department of Pediatric Cardiology, Cerrahpaşa Medical Faculty, Istanbul University, Istanbul, Turkey
*
Correspondence to: S. U. Atik, Department of Pediatric Cardiology, Cerrahpaşa Medical Faculty, Istanbul University, 34303 İstanbul, Turkey. Tel: +90 506 367 21 88; Fax: +90 212 632 00 50; E-mail: [email protected]
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Abstract

Rhabdomyoma is the most common cardiac tumour in children often associated with tuberous sclerosis. Arrhythmia caused by cardiac rhabdomyomas may be the initial sign of tuberous sclerosis. Rhabdomyomas unresponsive to other treatments could be successfully managed with everolimus, which has demonstrated benefit in tuberous sclerosis. We report a case of rhabdomyoma causing severe arrhythmia in a newborn managed successfully with everolimus.

Keywords

Rhabdomyomaarrhythmiaeverolimus
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 7 , October 2015 , pp. 1411 - 1414
Copyright
© Cambridge University Press 2014 

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