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Ebstein's malformation with covered defect of the ventricular septum

Published online by Cambridge University Press:  19 August 2008

Andreas Franke ,
Eberhard G. Mühler  and
Werner Hügel
Andreas Franke*
Affiliation:
From the Medical Clinic I, Klinikum der RWTH Aachen, Aachen
Eberhard G. Mühler
Affiliation:
From the Pediatric Cardiology, Klinikum der RWTH Aachen, Aachen
Werner Hügel
Affiliation:
Cardiothoracic Surgery, Klinikum der RWTH Aachen, Aachen
*
Dr. Andreas Franke, Medical Clinic I, Klinikum of the RWTH Aachen, Pauwelsstraße 30, D 52057 Aachen, Germany. Tel. 49-241-8089300/-301; Fax. 49-241-8888414.
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Abstract

The case of a 27-year-old male with Ebstein's malformation combined with a ventricular septal defect is reported. On its right ventricular side the defect was covered by the dysplastic septal tricuspid leaflet, creating a small chamber in continuity with the left ventricle, but without shunt into the remaining components of the right ventricle. The ventricular septal defect and a patent oval foramen were closed operatively after a cerebral embolic event to eliminate probable sources of thromboemboli preventing the inherent risks of life-long anticoagulation for a young patient. Intraoperative morphology confirmed the preoperative findings.

Keywords

Ebstein's malformationventricular septal defectcongenital heart disease
Type
Brief Reports
Information
Cardiology in the Young , Volume 6 , Issue 4 , October 1996 , pp. 341 - 343
Copyright
Copyright © Cambridge University Press 1996

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References

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