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Congenital right atrial diverticulum, atrial septal defect within the oval fossa, and complex pulmonary valvar obstruction in an infant with chromosome 8(p23.1) deletion

Published online by Cambridge University Press:  03 May 2005

Aungkana Gengsakul ,
Suvro S. Sett  and
Martin C. K. Hosking
Aungkana Gengsakul
Affiliation:
Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
Suvro S. Sett
Affiliation:
Division of Cardiothoracic Surgery, British Columbia Children's Hospital, Vancouver, Canada
Martin C. K. Hosking
Affiliation:
Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
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Abstract

We describe an unusual right atrial aneurysm, occurring with progressive obstruction of the right ventricular outflow tract and increasing cyanosis, in a nine-month-old boy with chromosome 8(p23.1) deletion. Surgical resection of the diverticulum, and relief of the right ventricular obstruction, was successful, although impairment of right ventricular compliance persists after 19 months follow-up.

Keywords

Chromosome deletioncongenital heart diseaseright ventricular obstruction
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 3 , June 2005 , pp. 306 - 308
Copyright
© 2005 Cambridge University Press

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