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A child with spontaneous resolution of idiopathic mid-aortic syndrome presented with dilated cardiomyopathy

Published online by Cambridge University Press:  02 December 2024

Beom Jae Kim ,
Gi Beom Kim Open the ORCID record for Gi Beom Kim [Opens in a new window]  and
Sang Yun Lee
Beom Jae Kim
Affiliation:
Department of Pediatrics, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, South Korea
Gi Beom Kim*
Affiliation:
Department of Pediatrics, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, South Korea
Sang Yun Lee
Affiliation:
Department of Pediatrics, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, South Korea
*
Corresponding author: Gi Beom Kim; Email: [email protected]
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Abstract

Mid-aortic syndrome is an uncommon vascular disease characterised by lower thoracic and upper abdominal aorta stenosis and can occur even in neonatal or infant periods. Here, we report an interesting case of a 2-month-old female with diffuse hypoplasia of the lower abdominal aorta and secondary dilated cardiomyopathy. In our patient, her abdominal aortic narrowing spontaneously normalised over time with the administration of consistent and goal-directed heart failure therapy, supporting adequate growth and natural recovery.

Keywords

Mid-aortic syndromecardiomyopathyanti-heart failure treatment
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 11 , November 2024 , pp. 2477 - 2479
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Copyright
© The Author(s), 2024. Published by Cambridge University Press

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