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‘Absent pulmonary valve’ syndrome associated with muscular ventricular septal defect and aneurysmal dilation of the ascending aorta

Published online by Cambridge University Press:  19 August 2008

Dennis Kececioglu
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
Omar Galal*
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
Fuad Abbag
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
*
Dr. Omar Galal, Section of Pediatric Cardiology, Cardiovascular Department (MBC 16), King Faisal Specialist Hospital and Research Center, PO Box 3354, Riyadh 11211, Saudi Arabia. Fax. (966-1) 442-7482.

Summary

A rare association of ‘absent pulmonary valve’ syndrome, midmuscular ventricular septal defect and aneurysmatic dilation of the ascending aorta without pathology of the aortic valve is described in a 10-month-old infant. The diagnosis was established by echocardiography and angiography.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1994

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References

1.McCaughan, BC, Danielson, GK, Driscoll, DJ,McGoon, DC. Tetralogy of Fallot with absent pulmonary valve: Early and late results of surgical treatment. J Thorac Cardiovasc Surg 1985; 89: 280287CrossRefGoogle ScholarPubMed
2.Ettedgui, JA, Sharland, GK, Chita, SK, Cook, A, Fagg, N, Allan, LD. Absent pulmonary valvesyndrome with ventricular sepral defect: Role of the arterial duct. Am J Cardiol 1990; 66: 233234.CrossRefGoogle Scholar
3.Fischer, DR, Neches, WH, Beerman, LB, Fricker, F, Siewers, RD, Lenox, CC, Park, SC. Tetralogy of Fallor with absent pulmonary valve. Analysis of 17 patients. Am J Cardiol 1984; 53: 14331437.CrossRefGoogle Scholar
4.Ruttenberg, H, Carey, LS, Adams, PA, Edwards, JE. Absence of the pulmonary valve in tetralogy of Fallot. Am J Roentgenol The Nucl Med 1964; 91: 500510.Google ScholarPubMed
5.McKusick, VA, Logue, RB, Bahnson, HT. Association of aortic valvular disease and cystic medial necrosis of the ascending aorta. Circulation 1957; 16: 188194.CrossRefGoogle ScholarPubMed
6.Zeit, RM, Cope, C, Lippmann, M. Compression of pulmonary artery by aortic aneurysm. J Am Med Assoc 1981; 246: 15861587.CrossRefGoogle ScholarPubMed
7.Bennet, DE, Cherry, JK. Bacterial infection of aorta aneurysms. Am J Surg 1967; 113: 321326.Google Scholar
8.Childers, R, McCrea, P. Absence of the pulmonary valve (a case occurring in the Marfan syndrome). Circulation 1964; 29: 598603.CrossRefGoogle ScholarPubMed
9.Bennet, DE, Cherry, JK. The natural history of traumatic aneurysms of the aorta. Surgery 1967; 61: 516523.Google Scholar