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Absence of the left ventricular myocardium in a newborn

Published online by Cambridge University Press:  19 August 2008

Angelika Lindinger ,
Yvonne Masur  and
Hans-Gerhard Limbach
Angelika Lindinger*
Affiliation:
From the Departments of Pediatric Cardiology and Pathology, the University of Hamburg/Soar
Yvonne Masur
Affiliation:
From the Departments of Pediatric Cardiology and Pathology, the University of Hamburg/Soar
Hans-Gerhard Limbach
Affiliation:
From the Departments of Pediatric Cardiology and Pathology, the University of Hamburg/Soar
*
Priv.-Doz. Dr. Angelika Lindinger, Abt. Pädiatrische Kardiologie, Universitätskliniken, D-66421 Homburg/Saar, Germany. Tel. 49 6841 16 8306; Fax. 49 6841 16 8330.
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Summary

Absence of myocardial fibers in the right ventricle is the essence of so-called Uhl's anomaly, which should be distinguished from the fatty replacement producing arrhythmogenic right ventricular dysplasia of the adolescent and young adult. In this report, we describe a newborn with nearly complete absence of the myocardium of the left ventricle. The infant died on the seventh day because of myocardial incompetence of the left ventricle, which was unable to open the aortic valve.

Keywords

Uhl's anomaly of the left ventricleabsence of left ventricular myocardiumnewborn
Type
Brief Reports
Information
Cardiology in the Young , Volume 6 , Issue 4 , October 1996 , pp. 344 - 347
Copyright
Copyright © Cambridge University Press 1996

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References

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