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A rare angiosarcoma: retiform haemangioendothelioma

Published online by Cambridge University Press:  05 September 2011

F O'Duffy ,
C Timon  and
M Toner
F O'Duffy*
Affiliation:
Department of Otorhinolaryngology, Royal Victoria Eye and Ear Hospital, Dublin, Ireland
C Timon
Affiliation:
Department of Otorhinolaryngology, Royal Victoria Eye and Ear Hospital, Dublin, Ireland
M Toner
Affiliation:
Department of Pathology, St James's Hospital, Dublin, Ireland
*
Address for correspondence: Mr Fergal O'Duffy, Royal Victoria Hospital, Adelaide Rd, Dublin 2, Ireland Fax: +353 14900643 E-mail: [email protected]
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Abstract

Objective:

We report the case of a rare angiosarcoma, retiform haemangioendothelioma, in an 18-year-old young man, which presented as a recurrent ulcerating lesion of the left pinna.

Method:

Case report and literature review of retiform haemangioendothelioma. This is a low grade angiosarcoma with a high local recurrence rate and low metastasis rate, and was first described in 1994 by Calonje et al.

Results:

This patient represents only the third report of lymph node metastasis in a case of retiform haemangioendothelioma. To date, 31 cases of the tumour have been reported. Histological diagnosis of this group of vascular neoplasms can be challenging, as their histopathological appearance is intermediate between haemangioma and angiosarcoma.

Conclusion:

Surgical excision remains the primary treatment modality, with adjuvant radiotherapy recommended in patients with large tumour size, local recurrence and lymph node metastasis, as seen in this case.

Keywords

EarPinnaRetiform HemangioendotheliomaHemangiosarcomaHemangiomaNeoplasm Metastasis
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 126 , Issue 2 , February 2012 , pp. 200 - 202
Copyright
Copyright © JLO (1984) Limited 2011

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References

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