Hostname: page-component-586b7cd67f-tf8b9 Total loading time: 0 Render date: 2024-11-24T18:04:30.114Z Has data issue: false hasContentIssue false

Punch-out lesion following regression of a large left ventricular outflow rhabdomyoma

Published online by Cambridge University Press:  29 August 2017

Ibrahim A. Abu Zahira
Affiliation:
Department of Pediatric Cardiology, Hadassah, Hebrew University Medical Center, Jerusalem, Israel
Amiram Nir*
Affiliation:
Department of Pediatric Cardiology, Hadassah, Hebrew University Medical Center, Jerusalem, Israel
*
Correspondence to: A. Nir, MD, Department of Pediatric Cardiology, Hadassah, Hebrew University Medical Center, Jerusalem 91120, Israel. Tel: +972 2 677 8132; Fax: +972 2 677 9114; E-mail: [email protected]

Abstracts

We report the case of a patient with rhabdomyoma of the left ventricular outflow tract, causing severe obstruction at birth. The tumour regressed completely by 6 years of age, leaving a punch-out lesion. The potential for spontaneous regression of these tumours and the formation of a myocardial lesion following rhabdomyoma regression are discussed.

Type
Brief Report
Copyright
© Cambridge University Press 2017 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Segal, I, Nir, A. Rhabdomyoma causing severe left ventricular outflow obstruction in a newborn. A management dilemma. Pediatr Cariol 2010; 31: 303305.Google Scholar
2. Ibrahim, CP, Thakker, P, Miller, PA, Barron, D.. Cardiac rhabdomyoma presenting as left ventricular outflow tract obstruction in a neonate. Interact Cardiovasc Thorac Surg 2003; 2: 572574.CrossRefGoogle ScholarPubMed
3. Breathnach, C, Pears, J, Franklin, O, Webb, D, McMahon, CJ. Rapid regression of left ventricular outflow tract rhabdomyoma after sirolimus therapy. Pediatrics 2014; 134: e1199e1202.Google Scholar
4. Aw, F, Goyer, I, Raboisson, MJ, Boutin, C, Major, P, Dahdah, N. Accelerated cardiac rhabdomyoma regression with everolimus in infants with tuberous sclerosis complex. Pediatr Cardiol 2017; 38: 394400.CrossRefGoogle ScholarPubMed
5. Hinton, RB, Prakash, A, Romp, RL, Krueger, DA, Knilans, TK. Cardiovascular manifestations of tuberous sclerosis complex and summary of the revised diagnostic criteria and surveillance and management recommendations from the International Tuberous Sclerosis Consensus Group. J Am Heart Assoc 2014; 3: e001493.Google Scholar
6. Bakan, S, Yahyayev, A, Bakan, AA, Dursun, M. Asymptomatic fatty changes in the myocardium of a patient with tuberous sclerosis. Pediatr Cardiol 2011; 32: 12161218.CrossRefGoogle ScholarPubMed