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Hypoplasia of the left heart with discordant ventriculoarterial connections

Published online by Cambridge University Press:  18 November 2005

Thomas Borth-Bruhns ,
Gerhard Ziemer  and
Michael Hofbeck
Thomas Borth-Bruhns
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Gerhard Ziemer
Affiliation:
Cardiothoracic Surgery, University Hospital, Tübingen, Germany
Michael Hofbeck
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
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Abstract

We report the rare combination of a severely hypoplastic left ventricle and discordant ventriculoarterial connections, with associated subpulmonary obstruction of the left ventricular outflow tract. The long tortuous arterial duct originated at an acute angle from the aorta, suggesting that the subpulmonary obstruction developed early in fetal life. Residual flow via the hypoplastic left ventricle to the pulmonary circulation after insertion of an aortopulmonary shunt resulted in haemodynamic deterioration, which was instantly reversed by closing the pulmonary trunk.

Keywords

Hypoplastic left heart syndrometransposition of the great arteriesfunctionally univentricular heart
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 6 , December 2005 , pp. 650 - 653
Copyright
© 2005 Cambridge University Press

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