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Congenital stenosis of pulmonary veins—failure to modify natural history by intraoperative placement of stents

Published online by Cambridge University Press:  19 August 2008

Seamus Cullen
Affiliation:
From the Departments of Paediatric Cardiology and Surgery, Royal Brompton National Heart & Lung Hospital and the Department of Paediatrics, National Heart & Lung Institute, London
Siew Yen Ho
Affiliation:
From the Departments of Paediatric Cardiology and Surgery, Royal Brompton National Heart & Lung Hospital and the Department of Paediatrics, National Heart & Lung Institute, London
Darryl Shore
Affiliation:
From the Departments of Paediatric Cardiology and Surgery, Royal Brompton National Heart & Lung Hospital and the Department of Paediatrics, National Heart & Lung Institute, London
Christopher Lincoln
Affiliation:
From the Departments of Paediatric Cardiology and Surgery, Royal Brompton National Heart & Lung Hospital and the Department of Paediatrics, National Heart & Lung Institute, London
Andrew Redington*
Affiliation:
From the Departments of Paediatric Cardiology and Surgery, Royal Brompton National Heart & Lung Hospital and the Department of Paediatrics, National Heart & Lung Institute, London
*
Dr. Andrew Redington, Department of Paediatric Cardiology, Royal Brompton National Heart & Lung Hospital, Sydney Street, London SW3 6NP, United Kingdom.

Abstract

Congenital pulmonary venous stenosis is a rare but important cause of pulmonary hypertension in infancy. The prognosis is uniformly poor, despite surgery and attempted balloon dilation of the narrowed veins. We performed intraoperative stenting of congenital pulmonary venous stenoses in two infants with initial clinical and hemodynamic improvement. Both patients subsequently died due to progressive pulmonary hypertension. Stenting of the pulmonary veins in this condition does not alter the natural history.

Type
Original Articles
Copyright
Copyright © Cambridge University Press 1994

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